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Huntington舞蹈病(ND)为常染色体显性遗传病。此病常在30~40岁时首次发病,而过早或过晚发病则罕见。在这些少见的病例中,青少年病例受到了极大的关注。青少年Huntington舞蹈病(JHD)有时被认为是由HD中分出来的一种类型,应将它和较常见的成年人临床型相区别。JHD依据发病年龄(AO)来划分,即HD在21岁以前发病者为JHD。JHD有几个明显的特征:青少年病例中有很多强直型HD。这些病例常常由其父亲遗传致病,似乎与孟德尔遗传学相矛盾。该
Huntington’s Chorea (ND) is an autosomal dominant disease. This disease often occurs for the first time in 30 to 40 years old, and premature or too late onset is rare. In these rare cases, teen cases have received a great deal of attention. Adolescents Huntington’s Chorea (JHD) is sometimes considered a type of component that is classified as HD and should be distinguished from the more common clinical forms of adults. JHD based on age of onset (AO) to divide, that is, HD in the age of 21 before the onset of JHD. JHD has several obvious characteristics: There are many cases of tetralogy HD in adolescents. These cases, often inherited by their father, appear to contradictory Mendelian genetics. This