噬血细胞综合征(HPS)又称噬血细胞淋巴组织细胞增生症(hemophagocytic lymphohistiocytosis,HLH),其临床特征为发热、肝脾肿大、全血细胞减少等。HPS分为原发性和继发性两大类。继发性HPS分为感染相关性HPS(infection-associated hemophagocytic syndrome,IAHS)、恶性相关性HPS Hemophagocytic syndrome (HPS), also known as hemophagocytic lymphohistiocytosis (HLH), the clinical features of fever, hepatosplenomegaly, pancytopenia and so on. HPS is divided into two major categories of primary and secondary. Secondary HPS is divided into infection-associated hemophagocytic syndrome (IAHS), malignant HPS