The clinical data of18 patients withPB fromApril1989 toApril2013 was analyzed retrospectively, including11 men and7 women, aged45 and76 years old(mean53 years).There were12 cases of PB occurring in right lung and other cases in left lung.Among them,3 patients had no symptoms, and15 patients displayed symptoms of cough, chest pain, asthenia or minor haemoptysis. Overall,11 patients had a preoperative diagnosis of lung cancer,7 patients were preoperatively diagnosed as the other diseases, which included lung benign tumor(n=5) and mediastinal mass (n=2).All patients received a radical resection.Six patients received postoperative cisplatin-based chemotherapy, and two patients received postoperative irradiation with the dose of55Gy. Histologically,14 cases of18 patients had biphasic pulmonary blastoma and four cases had well differentiated fetal adenocarcinoma.A total of12 patients died in a period of6-36 months after operation, and1 case was lost after2 years of follow up.The median survival time was19 months. PB is a rare primary lung malignant embryonal neoplasm.Despite its assumed embyonal origin, the tumor has a predilection for adults.A preoperative correct diagnosis is very difficult in spite of mod diagnostic imaging and biopsy techniques.Surgical resection is the main method for diagnosis and treatment.Postoperative chemotherapy or irradiation can help eliminate tumor remnants.Its prognosis is very poor, especially for the biphasic type.