Hirayama于 195 9年首次报道“青少年单侧上肢远端肌萎缩症” ,又称平山病。现就其临床表现、发病机制以及治疗等方面做如下综述。1　临床资料本综合症起病隐匿 ,男性占绝大多数 ,一般青少年期起病 ,15～ 2 5岁是发病高峰 ;病后 1～ 3年病情开始稳定 ,以后持续数十年无明显改变 Hirayama first reported in 1959 “young unilateral distal muscular atrophy”, also known as Ping Shan disease. Now on its clinical manifestations, pathogenesis and treatment, etc. made the following overview. 1 clinical data The syndrome occult onset, the vast majority of men, the general onset of adolescence, 15 to 25 years of age is the peak incidence; 1 to 3 years after the disease began to stabilize the condition for decades after no significant change