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骨髓增生异常综合征(MDS)是一组异质性多能干细胞疾患。特征是血细胞减少,红系、粒系和巨核系细胞成熟障碍和转变为急性白血病的倾向增加。FAB分型诊断和形态学标准是判断该病的自然过程和预后的基础。此病主要见于年长患者。然而,儿童原发性MDS由于比较少见以及命名上的混乱,诊断比较复杂。本文报道1979年1月～1991年9月,按FAB分型为
Myelodysplastic syndrome (MDS) is a group of heterogeneous pluripotent stem cell disorders. It is characterized by an increased propensity for cytopenias, erythroid, granulocytic and megakaryocytic maturation disorders and conversion to acute leukemia. FAB typing diagnosis and morphological criteria are the basis for judging the natural course and prognosis of the disease. The disease is mainly seen in older patients. However, due to the relatively rare and naming chaos in children with primary MDS, diagnosis is complicated. This article reports January 1979 ~ September 1991, according to FAB type