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目的 提高对淋巴管肌瘤病的影像学认识。方法 对 2例经病理证实的淋巴管肌瘤病患者的影像学表现及相关文献进行回顾研究。结果 2例均为女性 ,胸片示双肺弥漫网状结节影。HRCT表现为两肺均匀分布的薄壁囊状影 ,边缘清晰 ,大小不等 ,均伴有后腹膜淋巴结肿大 ,大者约 2 .5cm ,部分融合。 1例伴有右肾血管平滑肌瘤及腹膜后平滑肌瘤 ,呈均匀中等强化。结论 淋巴管肌瘤病是一种罕见的位于淋巴器官的平滑肌细胞病态增生的疾病。两肺广泛均匀分布的薄壁囊状影为其胸部HRCT特征。可同时伴有肾脏及腹膜后血管平滑肌瘤 ,腹膜后淋巴结肿大等
Objective To improve the imaging knowledge of lymphangiomyosarcoma. Methods Two cases of pathologically confirmed lymphangiomyoma were studied retrospectively. Results 2 cases were female, chest radiograph showed diffuse reticular nodules. HRCT showed uniform distribution of thin-walled cysts of both lungs, the edge of a clear, ranging in size, are accompanied by retroperitoneal lymph nodes, the largest of about 2.5cm, partial fusion. 1 case with right renal vascular smooth muscle tumor and retroperitoneal leiomyoma, was moderately moderate enhancement. Conclusion Lymphangiomyoma is a rare disease of hyperplasia of smooth muscle cells located in lymphoid organs. The thin-walled cystic shadow with broad and uniform distribution of both lungs is its chest HRCT feature. Can be accompanied by renal and retroperitoneal leiomyoma, retroperitoneal lymph nodes and so on