先天性肾上腺皮质增生症(CAH)为羟化酶缺乏性疾病.我院1981年4月～1986年12月共收治7例,占妇科同时期住院总数的0.695%.现报道如下.一、临床资料本组7例社会性别均为女性,年龄17～31岁.身长141～153cm;全身皮肤粗糙、多毛,除例5阴毛呈男性分布,其余均呈女性分 Congenital adrenal hyperplasia (CAH) is a hydroxylase deficiency disease in our hospital from April 1981 to December 1986 were treated in 7 cases, accounting for the total number of gynecological hospital 0.695%, are reported as follows. The data of 7 cases in this group were all female and were 17 to 31 years old and 141 to 153 cm in length. The skin of the whole body was rough and hirsutous. Except for case 5, the pubic hair was male and the others were female