患者男,13岁。自6岁始有发作性腹痛,伴粘液血便,便后腹痛缓解,同时发现口唇有米粒大小黑色素斑点。12岁后腹痛发作频繁、加重。有时可扪及包块,黑色素斑亦增大、增多,渐及手足。于1975年10月8日第一次住院,乙状结肠镜检发现降结肠下端有多个息肉,无蒂,即行息肉切除术。术后第二 Male patient, 13 years old. Since the age of six, there have been episodes of abdominal pain, with mucopuraemia, and relief of abdominal pain after the stool. At the same time, it has been found that the lips have spots of melanin of rice size. After 12 years of age, episodes of abdominal pain are frequent and aggravate. Occasionally, palpable masses can also be found. Melanosis also increases and increases. On October 8, 1975, he was hospitalized for the first time. His sigmoidoscopy revealed multiple polyps on the lower part of the descending colon. He had no pedicles and he underwent polypectomy. Second postoperative