报告我院１９８０～１９９３年手术的４例晚期病例，其中胰岛母细胞增殖症３例，胰岛细胞瘤１例。作者认为为了控制抽搐，避免继续加重脑损害，除强调早期诊断和早期手术外，对晚期病儿也应手术治疗，争取尽早稳定血糖水平。强调以９０％～９５％胰腺次全切除术为宜。迟发病例中可有部分为局部病变──胰岛细胞瘤，做局部切除可立即见效。 Report of our hospital from 1980 to 1993 surgery in 4 cases of advanced cases, of which 3 cases of islet cell proliferation, 1 case of islet cell tumor. The authors believe that in order to control seizures, to avoid further aggravating brain damage, in addition to emphasizing early diagnosis and early surgery, surgical treatment of children with advanced disease should also be sought, as soon as possible to stabilize blood sugar levels. Emphasis on 90% to 95% of the total subtotal pancreas appropriate. Delayed cases may have part of the local disease ─ ─ islet cell tumor, partial excision can be effective immediately.