报道11例 Huntington 舞蹈病,5例分布于4个家族中,3例家族史不详,3例为散发病例。男7例,女4例,发病年龄在28～58岁之间,平均40岁9个月。病程10个月～11年,平均5年9个月。多为隐袭起病。11例均有不自主舞蹈样动作和精神障碍,其中1例先有性格改变后出现舞蹈症.3例死亡(1例系自尽),余存活,但有半数生活不能自理。 Reported 11 cases of Huntington chorea, 5 cases distributed in 4 families, 3 family history is unknown, 3 cases were sporadic cases. There were 7 males and 4 females, with a mean age of 40 years and 9 months, ranging in age from 28 to 58 years. Duration of 10 months to 11 years, an average of 5 years and 9 months. Mostly insidious onset. Eleven patients had involuntary dance-like motions and mental disorders. One of the first cases had chorea after the change of personality. Three deaths (one suicide was caused by self-esteem) survived, but half of them could not take care of themselves.