1973年以来,文献上陆续报导了一个新的免疫异常综合证—免疫母细胞性淋巴腺病(IBL),或血管免疫母细胞性淋巴病伴异常蛋白血症(AILD)。其主要特点为B—淋巴细胞非肿瘤性增生,并转化为免疫母细胞,产生过多的免疫球蛋白,临床表现长期发热、多汗、体重减轻、皮疹、全身淋巴结及肝脾肿大,血中多株免疫球蛋白增高、和自体免 Since 1973, a new syndrome of immunodeficiency syndrome, immunoblastic lymphadenopathy (IBL), or angioimmunoblastic lymphadenopathy with anomalous proteinuria (AILD) has been reported in the literature. The main features of non-neoplastic B-lymphocytic proliferation, and transformed into immune cells, resulting in excessive immunoglobulin, clinical manifestations of long-term fever, hyperhidrosis, weight loss, rash, systemic lymph nodes and hepatosplenomegaly, blood In multiple strains of immunoglobulin increased, and self-exempt