房室结自律性心动过速(junctional ectopic tachycardia,JET)又称为先天性房室交界区无休止性心动过速、希氏束自律性心动过速等,是一种起源于房室交界区的自律性心动过速。儿童型患儿常自幼发病,自然病程较差,心动过速性心肌病出现早,对药物及非药物反应差,射频消融治疗难度大,风险高。本例患儿经射频消融降低异位起搏点自律性,配合药物治疗,效果良好。可作为本病治疗的借鉴。 Junctional ectopic tachycardia (JET), also known as congenital atrioventricular junctional area, restless tachycardia, His bundle self-paced tachycardia, etc., is a kind of originated in the atrioventricular junctional area Self-regulated tachycardia. Children with children often have childhood onset, poor natural history, early tachycardia cardiomyopathy, poor response to drugs and non-drugs, radiofrequency ablation treatment is difficult, high risk. This case of children with radio frequency ablation to reduce ectopic pacemaker self-discipline, with drug treatment, the effect is good. Can be used as a reference for the treatment of this disease.