胚胎发育不良性神经上皮肿瘤(DNT,WHOⅠ级)是中枢神经系统少见良性肿瘤,属神经元和混合性神经元-胶质肿瘤范畴。1988年由Daumas-Duport等首次命名。多见于儿童和青年,好发于大脑皮质,颞叶最为多见,其次为额叶,基底节、脑室、脑干、小脑、透明隔和胼胝体等亦有报道,肿瘤生长缓慢,临床主要表现为难治性癫,预后良好,术前明确诊断十分重要。典 Embryonic dysplastic neuroepithelial neoplasia (DNT, WHO grade Ⅰ) is a rare benign tumor of central nervous system, which belongs to the category of neurons and mixed neurons - glial tumors. 1988 first named by Daumas-Duport et al. More common in children and young people, occur in the cerebral cortex, the most common temporal lobe, followed by the frontal lobe, basal ganglia, ventricles, brainstem, cerebellum, transparent septum and corpus callosum have also been reported, the tumor growth is slow, the main clinical manifestations of difficult Governance epilepsy, a good prognosis, a clear preoperative diagnosis is very important. Code