目的探讨小儿重症法乐四联症外科手术技巧和术后并发症的预防及处理。方法连续无选择外科根治小儿重症法乐四联症４４例，采用回顾性的分析方法进行总结。结果本组病例无围手术期死亡，术后无残余分流，其中３例并发低心排综合征，经强心利尿治疗后痊愈。结论低温，低流量，减少心肌阻断时间，充分疏通右室流出道，防止残余分流及加强术后强心利尿治疗是取得良好手术效果的关键。 Objective To investigate the surgical techniques and postoperative complications in pediatric patients with tetralogy of Fallot. Methods A total of 44 cases of pediatric severe tetralogy of Fallot were surgically treated in our hospital without any surgical intervention and were retrospectively analyzed. Results There were no perioperative deaths in this group of patients. No residual shunt occurred after operation. Among them, 3 cases were complicated with low cardiac output syndrome and recovered after cardiac x-diuretic therapy. Conclusion Low temperature, low flow, reduce myocardial block time, and fully clear the right ventricular outflow tract to prevent residual shunt and strengthen postoperative cardiac diuretic treatment is the key to good surgical results.