该瘤是一种非常罕见的恶性肿瘤.世属文献仅有115例报道.在最近33年中,作者见到48例该肿瘤.几乎占成骨肉瘤的4%.在同时期软组织肉瘤中占的比例不到1%.平均年龄为51岁(6—80岁),3例小于30岁,男性23例,女性25例,肿瘤最常见的部位是大腿、臀 This tumor is a very rare malignancy. There are only 115 reports in the generic literature. In the last 33 years, the authors have seen 48 cases of this tumor, which account for almost 4% of osteosarcoma. It accounts for the same period of soft tissue sarcoma. The proportion is less than 1%. The average age is 51 years old (6-80 years old), 3 cases are less than 30 years old, 23 males and 25 females. The most common sites of tumors are thighs and buttocks.