周期性痉挛性动眼神经麻痹是一种较为罕见的眼科疾病 ,自 1 884年由Ｒａｍｐｏｌｄｉ[1] 首次报道以来 ,国外陆续报道数十例 ,国内报道 8例。 1 994年我科曾报道 1例[2 ] 。最近 ,我科又收治 1例 ,在临床表现及治疗方面与前例略有不同 ,现报道如下。病例报告　刘×× ,男 ,4岁 Cyclical spastic oculomotor palsy is a relatively rare ophthalmological disease that has reported dozens of cases in foreign countries and 8 cases in China since its first report by Rampoldi [1] in 1884. In 1994, our department had reported 1 case [2]. Recently, our department received another 1 case, the clinical manifestations and treatment slightly different from the previous case, are reported below. Case Report Liu × ×, male, 4 years old