鼻腔鼻窦腺样囊性癌(ACC)是来源于鼻腔鼻窦浆液腺及唾液腺的恶性肿瘤,它是一种生长缓慢低度恶性肿瘤,很少发生区域性淋巴结转移,能带瘤长期生存,但ACC具有明显的局部浸润性和远处转移的特征〔1〕。由于鼻腔鼻窦解剖复杂,部位隐蔽,鼻鼻窦ACC无典型临床症状和特异性影像学特征,早 Nasal Sinuses Adenoid cystic carcinoma (ACC) is a malignant tumor derived from the serous glands and salivary glands of the nasal sinuses. It is a slowly growing, low-grade malignant tumor with rare regional lymph node metastasis and long-term survival Has obvious characteristics of local infiltration and distant metastasis 〔1〕. Due to the complex anatomy of nasal sinuses, hidden parts, sinus acinar typical clinical symptoms and specific imaging features, as early as