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目的加强对肺上皮样血管内皮细胞瘤的认识,提高诊断率。方法通过对1例肺上皮样血管内皮瘤患者的诊治和文献复习,详细分析该病的病因、临床表现、诊断、鉴别诊断、治疗及预后等。结果该病病因不清,临床症状较少且轻微,影像学检查主要表现为两肺多发性结节影,可累及胸膜并出现胸腔积液;病理学检查主要特征是单细胞原始管腔结构;免疫组织化学提示内皮细胞源性。目前尚无有效治疗措施,患者预后介于良、恶性肿瘤之间。结论肺上皮样血管内皮瘤并双侧胸腔积液罕见,极易误诊,当肺部疾病治疗效果不佳时应警惕其可能性。
Objective To enhance the awareness of pulmonary epithelioid hemangiomas and improve the diagnosis rate. Methods A case of pulmonary epithelioid hemangioendothelioma in patients with diagnosis and literature review, a detailed analysis of the etiology, clinical manifestations, diagnosis, differential diagnosis, treatment and prognosis. Results The etiology of the disease was unclear. The clinical symptoms were mild and slight. The imaging findings mainly manifested as multiple nodules of both lungs, involving the pleura and pleural effusion. The primary features of the pathological examination were the single lumenal lumen structure. Immunohistochemistry suggests endothelial cell origin. There is no effective treatment, the prognosis of patients is between benign and malignant tumors. Conclusions Pulmonary epithelioid hemangioendothelioma with bilateral pleural effusion is rare and easily misdiagnosed, and should be wary of the possibility of poor response to lung disease.