本文报告2例独特的肉芽肿综合征患者,其主要表现为继发于弥漫性嗜酸性间质性肾炎的肾功能衰竭,双侧前房色素膜炎,骨髓肉芽肿,高丙种球蛋白血症和血沉加快。其中一例为14岁女孩,因双胁痛、间断腹痛、恶心、厌食与不适,尿中有蛋白、脓与管型,造影见肾脏增大,继之出现苍白、消瘦和肾功能恶 This article reports 2 patients with unique granulomatous syndrome, which is mainly manifested as renal failure secondary to diffuse eosinophilic interstitial nephritis, bilateral anterior uveitis, myelogenous granuloma, hypergammaglobulinemia And erythrocyte sedimentation rate faster. One of the cases was a 14-year-old girl with dystonia, intermittent abdominal pain, nausea, anorexia and discomfort, urinary protein, pus and tube type, angiography with increased kidneys, followed by paleness, weight loss and renal dysfunction