本文报告60例右室双出口的临床、血液动力学、X线及病理资料。根据心血管造影及手术所见,右室双出口可以分为四型,即室间隔缺损在:(1) 主动脉瓣下合并肺动脉瓣狭窄;(2) 主动脉瓣下无肺动脉瓣狭窄;(3) 肺动脉瓣下无肺动脉瓣狭窄;(4) 主动脉瓣和肺动脉瓣下有或无肺动脉瓣狭窄。临床诊断右室双出口十分困难,常被误诊为法乐氏四联症或艾森曼格综合征。在诊断中选择性心血管造影特别重要。一般来说,本病需要手术治疗。 This article reports 60 cases of right ventricular double outlet clinical, hemodynamic, X-ray and pathological data. According to cardiovascular angiography and surgery, the right ventricle double outlet can be divided into four types, namely, ventricular septal defect in: (a) aortic valve with pulmonary stenosis; (2) aortic valve without pulmonary stenosis; ( 3) No pulmonary stenosis under the pulmonary valve; (4) Aortic and pulmonary valve stenosis with or without pulmonary valve. Clinical diagnosis of right ventricular double outlet is very difficult, often misdiagnosed as tetralogy of Fallot or Eisenmenger syndrome. In the diagnosis of selective cardiovascular angiography is particularly important. In general, the disease requires surgery.