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目的:分析散发性脊髓血管母细胞瘤MRI特征。方法:回顾性分析6例经病理证实散发性脊髓血管母细胞瘤MRI表现,结合文献比较与Von Hippel-Lindau(VHL)病相关脊髓血管母细胞瘤MRI表现差异。结果:6例散发性脊髓血管母细胞瘤均为髓内单发病灶,其中3例位于胸髓,2例位于颈髓,1例同时累及延颈髓;病灶长径1.7-7.3cm。5例病灶为实性,1例为囊实性,肿瘤均位于脊髓背侧,边界清楚,肿瘤实性部分表现为以等或稍长T1、长T2信号为主的混杂信号,强化明显,囊实性病灶囊壁亦明显强化,1例胸髓病例邻近软脊膜线样强化的“尾征”;合并流空血管影、脊髓空洞各4例,1例囊实性肿瘤并囊内出血,矢状位T2加权图像见液-液平面。结论:散发性脊髓血管母细胞瘤MRI表现具有特征性,与VHL病相关脊髓血管母细胞瘤病灶常多发、体积较小,预后较差且易复发相区别。
Objective: To analyze MRI features of sporadic hemangioblastomas. Methods: The MRI manifestations of sporadic hemangioblastoma confirmed by pathology were retrospectively analyzed. The MRI findings of spinal cord hemangioblastoma correlated with Von Hippel-Lindau (VHL) were compared. Results: Six cases of sporadic hemangioblastoma were intramedullary single lesions, of which 3 cases were located in the thoracic cavity, 2 cases were located in the cervical cord and 1 case was involved in the extension of the cervical cord. The length of the lesion was 1.7-7.3 cm. Five lesions were solid and one was cystic. The tumors were all located on the dorsal surface of the spinal cord. The boundaries were clear. The solid part of the tumor appeared as a mixed signal with equal or slightly longer T1 and longer T2 signals. Solid lesions of the cystic wall was also significantly enhanced, 1 case of chest and spinal cord adjacent to the linear enhancement of the “tail levy”; with empty flow vascular shadow, 4 cases of syringomyelia, 1 case of cystic tumor and intracapsular hemorrhage , Sagittal T2 weighted images see liquid - liquid level. CONCLUSIONS: Spinal cord hemangioblastoma is characterized by MRI manifestations that are often differentiated from lesions associated with VHL-associated lesions of the hemangioblastoma, which are often small, of poor prognosis and of relapse.