目的 介绍一例原发性眶内恶性血管外皮细胞瘤外科治疗。方法 通过脑血管造影 ,先行血管内真丝栓塞 ,后行肿瘤切除 ,局部化疗及文献复习。结果 局部血管杂音和博动消失 ,肿瘤全切除。随访三年 ,视力正常 ,肿瘤未复发。病理学检查 ,血管内真丝异物形成血栓。病理报告为恶性血管外皮细胞瘤。结论 血管极其丰富之肿瘤先行血管内栓塞 ,后行肿瘤全切除术及局部化疗 ,安全、有效、可取 Objective To introduce a surgical treatment of primary orbital malignant hemangiopericytoma. Methods Cerebral angiography was used to evaluate the embolization of endovascular silk thread, followed by tumor resection, local chemotherapy and literature review. The results of local vascular murmur and Bo disappeared, tumor resection. Follow-up for three years, visual acuity, the tumor did not relapse. Pathological examination, intravascular silk foreign body formation thrombosis. Pathology report is malignant hemangiopericytoma. Conclusions Vascular tumors of the most abundant endovascular embolization, followed by total tumor resection and local chemotherapy, safe, effective, desirable