我院于1982年3月,经选择性右心室造影证实右室双出口两例,其X线征象典型,现结合文献复习报告和讨论如下。 病例报告 例1,男,25岁。自幼心悸气短,喜蹲踞,无晕厥史。查体:体温36.5℃,脉搏84次/分、血压112/80mmHg,呼吸24次/分。发育尚可,营养欠佳,口唇、颜面明显发绀,有杵状指趾。心前区隆起,胸骨左缘第4～5肋间可闻及三级吹风样收缩期杂音,P_2消失。化验:血红蛋白30.3g％、红细胞685万/mm~3,红细胞压积67容％。心电图:窦性心率、QRS电轴(+114°),不正常心电图,右心室肥厚劳损,右心房负 Our hospital in March 1982, confirmed by selective right ventricular double outlet right ventricle in two cases, the typical X-ray signs are combined with the literature review and discussion are as follows. Case report 1, male, 25 years old. Since childhood, palpitations shortness of breath, hi squat, no history of syncope. Physical examination: body temperature 36.5 ℃, pulse 84 beats / min, blood pressure 112 / 80mmHg, breathing 24 beats / min. Development is acceptable, poor nutrition, lips, face obvious cyanosis, clubbing toe. Anterior precinct uplift, sternal left intercostal space 4 to 5 can be heard and three-stage hair-style systolic murmur, P 2 disappeared. Assay: hemoglobin 30.3g%, erythrocytes 6850000 / mm ~ 3, hematocrit 67%. ECG: sinus heart rate, QRS axis (+ 114 °), abnormal ECG, right ventricular hypertrophy strain, right atrial negative