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目的:进一步认识眼型Behcet病的临床表现,有助于确诊及治疗。方法:回顾性总结2002年6月~2007年6月间,以眼部损害为主要表现来我院就诊的45例Behcet病患者的临床资料,从首发表现、眼部及眼外表现、眼底荧光血管造影(FFA)和临床疗效特点诸方面进行分析。结果:本组未见眼部损害为首发表现。首发临床表现以口腔溃疡居首位(80.0%),口腔溃疡发生率(100%)。FFA以视网膜主干血管及视盘渗漏为主者,病情较轻,预后良好;以视网膜微血管渗漏为主者,病势较重;伴视网膜出血及棉絮斑者,病情最为严重;表现为前部葡萄膜炎及角膜炎者预后较好。结论:对眼部及眼外病变的全面正确认识是及时诊断治疗Behcet病的关键。
Objective: To further understand the clinical manifestations of eye-shaped Behcet disease, which is helpful for diagnosis and treatment. Methods: The clinical data of 45 patients with Behcet’s disease treated by our hospital from June 2002 to June 2007 were reviewed retrospectively. First-line performance, ocular and extraocular conditions Angiography (FFA) and clinical efficacy characteristics of various aspects of the analysis. Results: No eye damage in this group was the first manifestation. The first clinical manifestations of oral ulcers in the first place (80.0%), the incidence of oral ulcers (100%). FFA to the main retinal blood vessels and optic disc leakage, mild disease, the prognosis is good; the main retinal microvascular leakage, the disease is severe; with retinal hemorrhage and cotton spots, the most serious condition; the performance of the front grapes Prophylaxis of meningitis and keratitis is better. Conclusion: A comprehensive and correct understanding of the ocular and extra-ocular lesions is the key to timely diagnosis and treatment of Behcet’s disease.