皮肤粘膜色素沉着——胃肠道多发性息肉综合征(Peutz—Jeghers Syndrome,简称PJS)为少见疾病;国内文献共报告22例,现将我们见到的一例结合国内资料作综合分析。患者,男,18岁,因腹部阵发性绞痛伴呕吐,便秘不排气16小时,1979年3月29日下午入院。患者自出生后即发现口唇、手足指趾掌侧有黑斑点,初为针尖大,随年龄增 Mucocutaneous pigmentation—Peutz-Jeghers Syndrome (PJS) is a rare disease; 22 cases have been reported in the domestic literature, and we have combined one case with domestic data for comprehensive analysis. The patient, male, 18 years old, had paroxysmal colic with vomiting, constipation did not vent for 16 hours, and was admitted to the hospital on the afternoon of March 29, 1979. After the birth, the patient noticed black spots on the lips and the palms of the fingers and toes, and the needles were large at the beginning and increased with age.