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恶性纤维组织细胞瘤(MFH)是少见的骨或软组织肿瘤,好发于四肢长骨,发生于颌骨及颌面软组织者罕见。 1 病历摘要例1,女,25岁。因左上颌部逐渐肿胀3个月,近1个来肿胀明显并伴有疼痛住院。检查:左上颌部明显肿胀,有压痛,左上颌2~8牙齿松动,前庭沟丰满,骨质变薄。X线检查:软组织肿胀,上颌窦密度增高,前壁、外侧壁及下壁均有破坏。临床诊断:左上颌骨恶性肿瘤。治疗:全麻下行左上颌骨次全切除术。术中见肿瘤充满上颌窦腔,质硬韧,除上壁外其它各壁均有破坏。术后病理报告:恶性纤维组织细胞瘤。术后10个月局部复发,行化疗,现带瘤生存。例2,男,7岁。左颞部软组织肿瘤,2
Malignant fibrous histiocytoma (MFH) is a rare bone or soft tissue tumor that occurs in the long bones of the extremities and is rare in the jaws and maxillofacial soft tissues. 1 Case summary 1 female, 25 years old. As the left upper jaw gradually swelled for 3 months, nearly one swelling was evident with pain in the hospital. Examination: The upper left maxilla is obviously swollen with tenderness. The upper left jaw has 2-8 loose teeth and the vestibular ramus is plump and thin. X-ray examination: soft tissue swelling, increased maxillary sinus density, destruction of the anterior wall, lateral wall, and inferior wall. Clinical diagnosis: Left upper jaw malignancy. Treatment: Subtotal resection of the left maxilla under general anesthesia. During the operation, the tumor was filled with a maxillary sinus cavity, which was hard and tough, and all other walls except the upper wall were damaged. Postoperative pathology report: malignant fibrous histiocytoma. After 10 months of local recurrence, chemotherapy, and now with tumor survival. Example 2, male, 7 years old. Left temporal soft tissue tumor, 2