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用类固醇激素及ACTH治疗小儿脱髓鞘疾病有一定疗效,已被临床证实。作者对2例年龄分别为9岁及10岁的多发性硬化症(MS)患儿,1例11岁的急性播散性脑脊髓炎(ADEM)患儿,应用甲基强地松龙冲击疗法,观察了对临床、脑电图、头部CT的影响:(1)冲击疗法开始后数日临床症状显著改善;(2)经1个月后脑电图慢波灶逐渐改善;(3)2例MS患儿头部CT所见,经冲击疗法后环状增强消失,仅残留低吸收区;(4)副作用小。上述结果说明,冲击疗法是治疗小儿脱髓鞘疾病安全、有效的治疗方法。冲击疗法即用甲基强地松龙每日30mg/kg,溶于
Steroid hormones and ACTH treatment of children with demyelinating disease has a certain effect, has been clinically confirmed. The authors of two cases of children aged 9 and 10 years of multiple sclerosis (MS), a 11-year-old children with acute disseminated encephalomyelitis (ADEM), application of methylprednisolone impact therapy , The effects on clinical, EEG and head CT were observed: (1) the clinical symptoms were significantly improved on the first few days after the start of the impact therapy; (2) the gradual improvement of the EEG slow-wave area after 1 month; (3) 2 Cases of MS seen in children with head CT, ring after ringing therapy disappeared, leaving only low absorption area; (4) side effects. The above results show that shock therapy is a safe and effective treatment for pediatric demyelinating diseases. Impact therapy that use methyl prednisolone daily 30mg / kg, dissolved in