Fabry病患者白质病变严重程度与性别的关系

来源 :世界核心医学期刊文摘(神经病学分册) | 被引量 : 0次 | 上传用户:starfox_vip
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In male patients with Fabry disease (FD), significant agerelated cerebral white matter lesions (WMLs) can be found. Although characteristic symptoms including cerebrovascular events are highly prevalent also in females with FD, cerebral structural changes have not been investigated in female FD patients yet. The authors quantified the WML load of 13 male and 14 age-matched female patients with FD and could demonstrate a comparably high frequency and severity of WMLs in both groups. In male patients with Fabry disease (FD), significant agerelated cerebral white matter lesions (WMLs) can be found. Although characteristic symptoms including cerebrovascular events are highly prevalent also in females with FD, cerebral structural changes have not been investigated in female FD patients yet The authors quantified the WML load of 13 male and 14 age-matched female patients with FD and could demonstrated a comparably high frequency and severity of WMLs in both groups.
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