心脏横纹肌瘤是婴儿期最常见的原发性心脏肿瘤 .其临床表现有心脏杂音、心律失常、心力衰竭、伴有结节性硬化症等 ,磁共振在临床诊断上的作用日益重要 .在组织学上 ,横纹肌瘤被认为是错构瘤 .一般采用保守治疗 ,只有当横纹肌瘤引起血流动学阻塞或心律紊乱时才采取手术治疗 Rhabdomyosarcoma of the heart is the most common primary cardiac tumor in infancy. Its clinical manifestations include heart murmurs, arrhythmia, heart failure, and tuberous sclerosis. Magnetic resonance imaging plays an increasingly important role in clinical diagnosis. In theory, rhabdomyoma is considered to be hamartoma. Conservative treatment is generally used. Surgery is only performed when rhabdomyosarcoma causes hemodynamic obstruction or arrhythmia.