Schuknecht( 1 989)报告先天性外耳道闭锁或狭窄伴胆脂瘤的发病率为 8% ,我科 1 985～ 1 997年收治 68例先天性耳畸形患者 ,伴有胆脂瘤者 1 9例 ,发病率为 2 7.9% ,临床误诊 1 5例。为使同道重视 ,现将其临床资料报告如下。1　资料和方法1 .1 　 临床资料1 9例先天性外耳道闭锁 Schuknecht (1989) reported that the incidence of congenital external auditory canal atresia or stenosis with cholesteatoma was 8%. Our department from 1985 to 1997, 68 cases of congenital ear malformation, with cholesteatoma in 19 cases, The incidence was 2 7.9%, clinical misdiagnosis of 15 cases. To make the same importance, now the clinical data reported as follows. 1 Materials and Methods 1.1 Clinical Information 19 cases of congenital external auditory canal atresia