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本文报道再生障碍性贫血(AA)102例的发病情况。慢性再生障碍性贫血(CAA)和重型再生障碍性贫血(SAA)的血象变化与临床表现的关系。CAA和重型再生障碍性贫血-Ⅱ型(SAA-Ⅱ)患者,住院治疗1~+月至1~+年,追踪半年以上共61例,经雄激素,SSL(康力龙、一叶萩碱、左旋咪唑),强的松等治疗,有效23例(37.7%),无效32例(52.46%),死亡6例(9.84%)。重型再生障碍性贫血-Ⅰ型(SAA-Ⅰ)共32例,经皮质激素、输血及抗感染等治疗1~+天至3月有效2例(6.25%),无效13例(40.63%),死亡17例(53.12%)。主要死因为颅内出血及败血症。
This article reports the incidence of aplastic anemia (AA) in 102 cases. The Relationship between Hemogram Changes and Clinical Features of Chronic Aplastic Anemia (CAA) and Severe Aplastic Anemia (SAA). CAA and patients with severe aplastic anemia-type II (SAA-II), were hospitalized for 1 month to 1 month and followed up for 1 year and up to 61 years. Sixty-one patients were followed up for more than six months. After androgen, SSL, Imidazole) and prednisolone, effective in 23 cases (37.7%), ineffective in 32 cases (52.46%) and death in 6 cases (9.84%). A total of 32 patients with severe aplastic anemia-type Ⅰ (SAA-Ⅰ) were treated with corticosteroids, transfusion and anti-infective therapy for 2 days (6.25%) and ineffective in 13 cases (40.63% 17 cases died (53.12%). The main cause of death is intracranial hemorrhage and sepsis.