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患儿,男,3岁,甘肃籍,居住林场。因反复发热、面色苍白1年5个月,加重3个月,于1995年10月23日入院。曾在当地多家医院先后行4次骨穿,多次以病毒感染、粒细胞缺乏症住院治疗,病情无明显缓解。患病来伴咳嗽、多汗、乏力、纳差、进行性消瘦。查体:体温36.9℃,身高83cm,体重11kg,发育营养较差,贫血貌。全身皮肤松弛,方颅,双肺呼吸音粗,肺底可闻及少许湿啰音,心脏各瓣膜听诊区可闻及3/6级粗糙收缩期杂音;蛙状腹,皮下脂肪菲薄,腹部无压痛、反跳痛,肝肋下5.5cm,脾肋下7.0cm,移动性浊音阴性。双下肢轻度水肿。辅助检查:血红蛋
Children, male, 3 years old, Gansu Ji, living forest. Due to repeated fever, pale 1 year and 5 months, increased 3 months, on October 23, 1995 admission. Many hospitals in the local has 4 times the bone wear, many times to virus infection, agranulocytosis hospitalized, the disease was not significantly alleviated. Ill with cough, sweating, fatigue, anorexia, progressive weight loss. Physical examination: body temperature 36.9 ℃, height 83cm, weight 11kg, poor nutrition, anemia appearance. Systemic skin relaxation, square skull, lung breath sounds thick, lungs can be heard and a little wet rales, heart valve auscultation area can be heard and 3/6 rough systolic murmur; frog belly, subcutaneous fat meager, abdomen Tenderness, rebound tenderness, liver ribs 5.5cm, spleen ribs 7.0cm, mobility dullness negative. Lower extremity mild edema. Auxiliary examination: hemoglobin