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目的:提高对肾脏炎症性肌纤维母细胞瘤(IMT)的认识。方法:报告1例肾脏IMT病例,结合文献探讨该病的病因、病理、临床表现、治疗及预后。结果:患者,男,52岁,因“上腹部疼痛10天,加重伴呕吐8天”入院。影像学检查提示右肾下极占位性病变。手术切除右肾,术后病理诊断为右肾炎症性肌纤维母细胞肿瘤。术后3月随访未见复发。结论:肾脏IMT临床罕见,易误诊为肾癌等疾病,确诊需依靠病理学诊断。手术切除肾脏是目前较为有效的方法。
Objective: To improve the understanding of renal inflammatory myofibroblastic tumor (IMT). Methods: One case of renal IMT was reported, and the etiology, pathology, clinical manifestation, treatment and prognosis of the disease were discussed. Results: The patient, male, 52 years old, was hospitalized because of “upper abdominal pain for 10 days, aggravated with vomiting for 8 days.” Imaging examination prompted the right subrenal pole occupying lesions. Surgical removal of the right kidney, postoperative pathological diagnosis of right renal myofibroblastic tumor. No follow-up after 3 months of recurrence. Conclusion: Kidney IMT is clinically rare and easily misdiagnosed as kidney cancer and other diseases. Diagnosis depends on pathological diagnosis. Surgical removal of the kidneys is currently a more effective method.