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目的探讨血管瘤病的临床病理特点及鉴别诊断。方法复习4例血管瘤病患者的临床资料,标本常规石蜡切片、HE染色和EnVision免疫组化染色。结果4例患者中,女性3例,男性1例,发病年龄小,病变累及范围广。镜下见增生的血管弥漫浸润性生长,并可垂直累及皮下、肌肉和骨组织,可见特征性的静脉血管壁内或附着于静脉壁上花束状排列的不规则血管簇。增生的血管CD31、CD34和FⅧ(+)。结论血管瘤病是一种少见的良性软组织疾病,临床累及范围广,主要发生于儿童和青少年,诊断时必须强调临床病史与病理形态相结合。
Objective To investigate the clinicopathological characteristics and differential diagnosis of hemangiomatosis. Methods The clinical data of 4 patients with hemangiomatosis were reviewed. Paraffin sections, HE staining and EnVision immunohistochemical staining were performed. Results Among the 4 patients, 3 were female and 1 was male, with a small age of onset and a wide range of lesions. Microscopic see proliferative vascular diffuse infiltrative growth, and can be vertically involving the subcutaneous, muscle and bone tissue, showing characteristic vein wall or attached to the veins on the wall-like arrangement of irregular vascular clusters. Proliferating blood vessels CD31, CD34 and FⅧ (+). Conclusion Hemangiomatosis is a rare benign soft tissue disease with a wide range of clinical involvement, mainly in children and adolescents. The diagnosis must be based on the combination of clinical history and pathology.