本文报告在一家族中发生一种罕见的综合征,在其20个成员中,竟有7人发病,计男3、女4。其表现为毛囊性皮肤萎缩(7例)、基底细胞癌(5例)、局部无汗(6例)、全身出汗减少(3例)及出生后不久面部发生湿疹(4例)。 This article reports that a rare syndrome occurs in a family. Of the 20 members, as many as 7 have a history of 3 males and 4 females. It manifested as follicular skin atrophy (7 cases), basal cell carcinoma (5 cases), local non-sweat (6 cases), reduced body sweating (3 cases), and eczema on the face shortly after birth (4 cases).