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颅内原发生殖细胞瘤好发于松果体区和鞍区 ,而发生于基底节和丘脑区者少见 ,该病基本上只发生在男孩 ,除偏瘫为主要表现外 ,还可以有智力下降和语言障碍等。MR和CT示病变虽然体积比较大 ,但是病变周围水肿并不严重 ;边界不规则 ;可以有轻到中度的不均匀强化 ,可合并囊变 ,钙化 ,出血 ,患侧大脑半球萎缩等。同颅内其它部位生殖细胞瘤一样对放疗十分敏感 ,基本上可以达到治愈 ;此外可以应用联合化疗 ;手术和活检对明确诊断有帮助
Intracranial germ cell tumors occur in the pineal region and the saddle area, while in the basal ganglia and thalamus are rare, the disease occurs only in boys, in addition to hemiplegia as the main performance, but also can have mental decline And language barriers. Although MR and CT showed lesion volume is relatively large, but the edema around the lesion is not serious; the border is irregular; can have mild to moderate heterogeneous enhancement, cystic degeneration, calcification, hemorrhage, ipsilateral cerebral hemisphere shrinkage. Like other parts of the intracranial germ cell tumor is very sensitive to radiotherapy, basically can be cured; in addition can be combined with chemotherapy; surgery and biopsy helpful to confirm the diagnosis