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虽然室性心动过速和心室颤动常见于冠状动脉病变的成年人,但也可发生于年轻人,包括先天性心脏病手术后,各种心脏疾病,自主神经平衡失调,服用某些药物以及无心脏病者。本文报道18名有室性心动过速和/或心室颤动的年轻病人的临床和电生理学。患者男、女性各9例,年龄4天~24岁(平均16.6岁),随访4~70(平均22.4)个月。12例有器质性心脏病,计二尖瓣脱垂4例,充血性心肌病3例,心肌炎2例,QT间期延长综合征1例,室间隔缺损1例,原因不明的心脏病1例。6例反复发作室性心动过速,经药物控制后未能发现心脏病变,其中1例为扭转型室性心动过速伴晕厥,有不明原因的低血钾(2.2毫当量/升)。
Although ventricular tachycardia and ventricular fibrillation are common in adults with coronary artery disease, they can also occur in young adults, including those with congenital heart disease, various heart conditions, autonomic imbalance, taking certain medications, Dirty patients. This article reports the clinical and electrophysiology of 18 young patients with ventricular tachycardia and / or ventricular fibrillation. Nine patients were male and female, aged from 4 days to 24 years (average 16.6 years). The patients were followed up for 4 to 70 (average 22.4) months. 12 patients had organic heart disease, including 4 cases of mitral valve prolapse, 3 cases of congestive cardiomyopathy, 2 cases of myocarditis, QT prolongation syndrome in 1 case, ventricular septal defect in 1 case, unexplained heart disease 1 example. Six patients had recurrent ventricular tachycardia and no heart disease was found after drug control. One patient had torsades decussation and syncope with unexplained hypokalemia (2.2 meq / l).