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地中海贫血是我国长江以南常见的单基因遗传性血液病,血红蛋白H(hemoglobin H,HbH)病是能生存下来的α地中海贫血个体中最严重的一种[1]。由于其特殊的发病机制及临床表现,目前对妊娠合并HbH病患者的孕期管理及治疗缺乏经验,并因此影响母婴的妊娠结局。本研究通过分析作者医院5年来收治的妊娠
Thalassemia is a common monogenic hereditary blood disease common to the south of the Yangtze River in China. Hemoglobin H (HbH) is the most severe form of alpha thalassemia that can survive [1]. Due to its special pathogenesis and clinical manifestations, there is currently a lack of experience in the management and treatment of pregnancy during pregnancy with HbH and thus affecting the pregnancy outcome of both mother and child. This study analyzed the author’s hospital for 5 years of pregnancy