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目的回顾性分析恶性外周神经鞘膜瘤的CT和MRI表现,提高对该病的诊断准确性。方法搜集恶性外周神经鞘膜瘤病人12例,术前均进行了CT或MRI检查。结果CT表现平扫上为等、低密度混合的软组织肿块影,外形不规则,边界清楚(n=9)或模糊(n=3);增强扫描时呈不均性强化,坏死区不强化。MRI表现边界模糊,信号混杂。T1WI序列上多与肌肉等信号(n=11),内示局灶性长T1信号影;T2WI抑脂序列上以略高信号为主,边界清楚(n=2)或模糊(n=10),内示局灶性长T2信号,周围软组织浸润表现为片状高信号;增强扫描时呈不均性强化。结论恶性外周神经鞘膜瘤的CT和MRI表现具有一定的特征性。
Objective To retrospectively analyze the CT and MRI findings of malignant peripheral nerve sheath tumor to improve the diagnostic accuracy of the disease. Methods Twelve patients with malignant peripheral nerve sheath tumor were collected and examined by CT or MRI before operation. Results The CT findings were equal and low density mixed soft tissue mass with irregular shape, clear border (n = 9) or blurred (n = 3). The enhancement scan showed uneven enhancement and the necrotic area was not enhanced. MRI performance blurred borders, mixed signals. T1WI sequence of multiple and muscle signals (n = 11), showing focal long T1 signal shadow; T2WI suppression sequence with a slightly higher signal-based, clear boundary (n = 2) or fuzzy (n = 10) Within the long focal T2 signal showed soft tissue infiltration showed flaky high signal; enhanced scanning showed uneven enhancement. Conclusion CT and MRI findings of malignant peripheral nerve sheath tumor have certain characteristics.