论文部分内容阅读
目的探讨颅内非松果体区生殖细胞瘤的循证诊断和治疗。方法1例丘脑区病变首发尿崩经实验性放疗证实;基底节区1例经立体定向活检病理证实;鞍区3例经手术及病理确诊,2例次全切除,1例部分切除。均接受病灶+全脑放疗。结果1例无症状存活13年余,3例明显改善,1例死于肿瘤颅内、脊髓广泛种植转移。结论颅内非松果体区生殖细胞瘤的确诊依靠病理诊断,实验性放疗、化疗适用于有手术禁忌和不同意手术的病人,正规放疗是提高疗效的重要措施。
Objective To investigate the evidence-based diagnosis and treatment of intracranial non-pineal germ cell tumors. Methods One case of thalamic brain lesions confirmed by experimental radiotherapy was confirmed by experimental radiotherapy. One case of basal ganglia was confirmed by stereotactic biopsy. Three cases of sella were confirmed by operation and pathology. Two cases were subtotally resected and one case was partially resected. All lesions + whole brain radiotherapy. Results 1 case of asymptomatic survival of more than 13 years, 3 patients improved significantly, 1 patient died of intracranial tumors, extensive spinal cord metastasis. Conclusions The diagnosis of intracranial non-pineal region germinomas depends on pathological diagnosis. Experimental radiotherapy and chemotherapy are suitable for patients with contraindications of surgery and disagreeing with surgery. Regular radiotherapy is an important measure to improve curative effect.