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视网膜色素变性为致盲眼病,与遗传有关。笔者1978年收集10家系,计10例行尾骨切除术者;1983年以来又收集15家系,其中二家系同代中有二人患病,计17例;共25家系,27例。现分析如下。一、临床资料分析 (一)一般资料:本组男19例,女8例,男:女=2.4:1。27例全部为双眼患病。夜盲开始时间为10岁以下11例,11~20岁6例,21~30岁5例,31岁以上3例,不明2例。 (二)年龄与视力的关系见附表。
Retinal pigment degeneration caused by blindness, and genetic. The author collected 10 departments in 1978, accounting for 10 cases of coccyx resection; since 1983, 15 families were collected, of which two families in the same period, two were ill, accounting for 17 cases; a total of 25 lines, 27 cases. Analysis is as follows. First, the clinical data analysis (a) General Information: The group of 19 males and 8 females, males: females = 2.4: 1.27 cases of all binocular disease. Night blindness began in 11 cases under 10 years of age, 11 to 20 years in 6 cases, 21 to 30 years in 5 cases, 31 years of age in 3 cases, unknown in 2 cases. (B) the relationship between age and vision see schedule.