论文部分内容阅读
5例中,年龄4月、1岁、11岁各1例,2~3岁2例,男4例,女1例,发热,多饮、多尿及皮肤黄褐疹各3例,突眼3例,长期误诊为骨髓炎的大腿根部疼痛1例,5例头部均可扪及囊性包块及骨缺损,肝脾Ⅱ°肿大2例,Ⅲ°肿大1例。5例白细胞计数均>1×10~9/L,>2×10~9/L3例,Hb均<100g/L,其中<60g/L3例,1例周围血中检出9%的泡沫细胞。骨穿4例,2例为正常骨髓象,增生性贫血象及
In 5 cases, there were 1 case of 1 year old and 11 years old, 2 cases of 2 to 3 years old, 4 cases of male and 1 female, 3 cases of fever, polydipsia, polyuria and skin yellow rash. The exophthalmos 3 cases, long-term misdiagnosed as osteomyelitis in the thigh pain in 1 case, 5 cases of palpable head palpable cystic mass and bone defects, liver and spleen Ⅱ ° enlargement in 2 cases, Ⅲ ° enlargement in 1 case. 5 cases of white blood cell count were> 1 × 10 ~ 9 / L,> 2 × 10 ~ 9 / L3 cases, Hb were less than 100g / L, of which <60g / L3 cases, 1 case of peripheral blood was detected 9% foam cells . Bone wear in 4 cases, 2 cases of normal bone marrow, hyperplastic anemia and as