心脏损害是特发性炎症性肌病死亡和致残的重要原因。然而,心力衰竭、传导异常及冠心病等临床心血管表现相对少见,非特异性的心电图显示的传导异常及心律失常却很常见。事实上,这些心血管表现或多或少与心肌纤维化及小血管平滑肌增生相关,可致特发性炎症性肌病患者的死亡。因此,有必要推荐特发性炎症性肌病患者进行常规而全面的心脏评估。 Cardiac damage is an important cause of death and disability of idiopathic inflammatory myopathies. However, clinical cardiovascular manifestations such as heart failure, conduction abnormalities, and coronary heart disease are relatively rare. Non-specific ECGs are common for conduction abnormalities and arrhythmias. In fact, these cardiovascular manifestations are more or less associated with myocardial fibrosis and small-vessel smooth muscle hyperplasia and can cause death in patients with idiopathic inflammatory myopathies. Therefore, it is necessary to recommend routine and comprehensive cardiac assessment in patients with idiopathic inflammatory myopathies.