论文部分内容阅读
Sipple’s综合征属于多发性内分泌腺瘤(MEN)Ⅱ型,即肾上腺嗜铬细胞瘤合并甲状腺髓样癌,临床上比较罕见.现报告1例.患者,女,28岁.1981年开始出现阵发性心悸、胸闷、头痛、头晕、双手颤抖,伴月经周期紊乱,经色黯,量少.在当地医院经内科治疗无好转,诊断不明.1991年发现右侧甲状腺肿瘤,在当地医院行肿瘤摘除术,病理报告为甲状腺髓样癌.遂在手术后3个月再行右侧甲状腺全切除+双侧颈淋巴结改良清扫术.术后仍有心悸、胸闷、头痛.1993年3月B超发
Sipple’s syndrome is a type of multiple endocrine adenoma (MEN) type II, that is, adrenal pheochromocytoma with medullary thyroid carcinoma, is rare in clinical practice. It is reported in 1 case. The patient, female, 28 years old, began to appear in 1981 Heart palpitations, chest tightness, headache, dizziness, hands trembling, with menstrual cycle disorders, by color palpitations, small amount. In the local hospital after medical treatment has not improved, the diagnosis is unknown. In 1991, the right thyroid tumor was found and the tumor was removed at the local hospital. The surgical and pathological reports were medullary thyroid carcinoma. The hernia was removed 3 months after the operation and the right thyroid gland was removed and the bilateral neck lymph nodes were improved. There was still palpitation, chest tightness, and headache after the operation. In March of 1993, B ultrasound was performed.