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非典型畸胎样/横纹肌样肿瘤(ATRT)是以横纹肌样形态及SMARCB1(INI1)表达缺失为特征的脑肿瘤。筛状神经上皮性肿瘤(CRINETs)为筛状生长模式伴有SMARCB1表达缺失的罕见非横纹肌样脑肿瘤。小的病例系列报道提示CRINETs可能具有相对良好的预后,然而长期预后还不清
Atypical teratoid / rhabdomyosarcoma (ATRT) is a brain tumor characterized by a rhabdomyosarcoma-like morphology and a loss of expression of SMARCB1 (INI1). Screening neuroepithelial neoplasms (CRINETs) are rare, non-rhabdomyoid brain tumors with a lack of SMARCB1 expression in a mesh-like growth pattern. Small series of reports suggest that CRINETs may have a relatively good prognosis, however, long-term prognosis is unclear