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患儿男,3岁5个月,入院前一天开始无任何诱因出现发热伴抽风,每次抽3-4分钟,间隔1-2分钟,约5-6小时后出现昏迷。在入院前两个月曾抽风两次,表现与本次相同,当时否认发热,传染病及脑外伤等疾病。父母非近亲结婚。母在孕期及分娩期无异常。查体T38.8℃P130、R24。发育营养较差,意识不清,双瞳孔光反应差,前囱未闭约1.5×1.5cm~2方颅,颅缝未闭。咽红、串珠肋、有肋软沟。双肺散在干性罗音。肝右肋下1cm、边锐、质软、“O”形腿,腹壁反射和提睾反射均阴性。其他各系统检查均无其他病理征。wBC1.5万、St2%、S66%、L28%、M2%、异型淋巴2%;c、s、f压力24滴/分,蛋白定量10mg%,糖68mg%,氯化物770mg%。血糖63mg%。肝功TTT9u,SGPT184u。血钙10mg%,血磷3.2mg%,AKP21.5u。其余化验无阳性结果。入院后查CO_2CP示酸中毒,给予
Children, male, 3 years and 5 months, one day before admission, there is no incentive to start with fever and ventilation, each pumping 3-4 minutes, 1-2 minutes intervals, about 5-6 hours after the coma. In the first two months before admission, he had twice aspirated the air, showing the same as this one. He denied any fever, infectious diseases and traumatic brain injury. Parents marry non-relatives. Mother during pregnancy and childbirth no abnormalities. Physical examination T38.8 ℃ P130, R24. Developmental nutrition is poor, unconsciousness, poor pupil light response, anterior chimney about 1.5 × 1.5cm ~ 2 square cranio-cranial septum. Throat, beaded, ribbed soft ditch. Lung scattered in the dry rales. Liver right rib 1cm, while the sharp, soft, “O” -shaped legs, abdominal reflex and cremasteric reflex were negative. Other system checks have no other pathological sign. wBC1.5 million, St2%, S66%, L28%, M2%, atypical lymph 2%; c, s, f pressure 24 drops / min, protein content 10mg%, sugar 68mg%, chloride 770mg%. Blood sugar 63mg%. Liver function TTT9u, SGPT184u. Calcium 10mg%, phosphorus 3.2mg%, AKP21.5u. The remaining test no positive results. Check after admission CO_2CP acidosis, given