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目的:探讨胚胎发育不良性神经上皮肿瘤(dysembryoplastic neuroepithelial tumor,DNET)的CT和MRI表现,以提高对本病的认识。方法:回顾性分析经病理证实的11例DNET的临床及影像学资料。11例中7例行CT平扫;11例均行常规MRI检查,2例行MR波谱检查。结果:患者以癫痫小发作为临床表现,神经系统检查无阳性体征。11例DNET中7例位于额叶,3例位于颞叶,1例位于顶叶;病变均位于皮层区。7例患者的CT像上6例呈均匀低密度,1例呈低、等混杂密度,均未见钙化,4例可见邻近骨质变薄。MRI上病变呈均匀或不均匀长T1、长T2信号,仅1例见周围轻度水肿,余10例均无明显的占位效应和周围水肿;增强检查10例无明显强化,1例可见分隔轻度强化,其中7例肿瘤形态呈三角形或楔形。结论:DNET的影像学表现具有特征性,结合临床及影像学表现,可以在术前对DNET做出正确诊断。
Objective: To investigate the CT and MRI findings of dysembryoplastic neuroepithelial tumor (DNET) in order to improve the understanding of this disease. Methods: The clinical and imaging data of 11 cases of pathologically confirmed DNET were retrospectively analyzed. Among the 11 cases, 7 cases underwent CT scan. All 11 cases underwent routine MRI examination and 2 cases underwent MR examination. Results: Patients with epilepsy as a clinical manifestation of minor attacks, neurological examination without positive signs. Seven of the 11 DNETs were located in the frontal lobe, 3 in the temporal lobe and 1 in the parietal lobe. The lesions were located in the cortex. The CT images of 7 patients showed a uniform low density in 6 cases and a low, mixed density in 1 case. No calcification was found in the 7 cases. Thinning of the adjacent bone was seen in 4 cases. MRI lesions were uniform or uneven long T1, T2 signal, only 1 case of see mild edema around, the remaining 10 cases had no significant space-occupying effect and peripheral edema; enhanced examination of 10 cases without significant enhancement, 1 case can be seen separated Mild enhancement, of which 7 cases of tumor morphology was triangular or wedge. Conclusion: DNET has the characteristics of imaging findings, combined with clinical and imaging findings, DNET can be correctly diagnosed before surgery.