腺泡状软组织肉瘤(alveolar soft-part sarcoma,ASPS)比较少见,约占全部软组织肉瘤的0.5%~1%[1]。其具有特征性的组织学表现、未知的组织学起源和分化方向及不可预知的生物学行为。多发生于下肢或胸背部、臀部等深部软组织,散发病例报告也见于女性生殖道、肺、纵隔、骨、宫颈、后腹膜、鼻窦及心脏等部位[2],但发生于乳腺非常罕见。本文报道1例乳腺ASPS,并结合文献复习探 Alveolar soft-tissue sarcoma (alveolar soft-part sarcoma, ASPS) is relatively rare, accounting for about 0.5% to 1% of all soft tissue sarcoma [1]. It has characteristic histological manifestations, unknown histological origins and directions of differentiation, and unpredictable biological behavior. Occurred in the lower limbs or chest and chest, buttocks and other deep soft tissue, sporadic cases also found in female reproductive tract, lung, mediastinum, bone, cervix, retroperitoneal, sinus and heart and other parts [2], but occurred in the breast is very rare. This article reports 1 case of breast ASPS, combined with the literature review exploration