输尿管纤维上皮性息肉是中胚层来源的少见的良性肿瘤,是儿童肾盂积水极少见的原因。它通常引起部分输尿管阻塞,不会产生肾功能损害。优先考虑的治疗方法是在保存肾单位的情况下行内窥镜或者外科息肉切除术。笔者描述1例青少年患者,其输尿管远端巨大纤维上皮性息肉导致输尿管完全性阻塞,引起左肾盂积水和左肾功能损害。输尿管良性肿瘤导致肾单位的损害,这是极为罕见的报道。 Ureteral fibroepithelial polyps are rare benign tumors of the mesodermal origin and are a very rare cause of hydronephrosis in children. It usually causes partial obstruction of the ureter and does not produce impaired renal function. The preferred treatment is endoscopic or surgical polypectomy with the nephron preserved. I describe a case of adolescent patients, the distal ureteral giant fibroal epithelial polyp causes complete obstruction of the ureter, causing left renal pelvis and left renal dysfunction. Ureteral benign tumors lead to nephron damage, which is extremely rare.