我国先天性小耳畸形发病率约为 0 .0 85‰ ,其中多伴发其它畸形 ,以颌面部多见[1] 。我科于 2 0 0 2年 1月收治 1例小耳畸形伴咽峡畸形及面神经麻痹的患者 ,报告如下。患者 ,女 ,2 1岁 ,出生后发现右侧耳廓小 ,上半部卷曲 ;左侧耳廓仅残留约黄豆大小赘生物 ,无外耳道。双耳听力 The incidence of congenital malformations in our country is about 0.085 ‰, many of them with other malformations, with maxillofacial more common [1]. In January 2002, our department admitted a patient with small ear malformations with pharyngeal girth deformity and facial paralysis, the report is as follows. Patients, female, 21 years old, was found after birth, a small ear on the right, the upper part of the curl; the left ear ear left only about the size of soybean vegetation, no external auditory canal. Binaural hearing